Table 2.

Hereditary Breast Cancer Syndromes

Syndrome Known susceptibility gene(s)
Site-specific breast cancer BRCA1, BRCA2
Site-specific ovarian cancer BRCA1
Breast–ovarian cancer BRCA1,BRCA2
Cowden syndrome PTEN
Li-Fraumeni syndrome p53
HNPCC (Lynch syndrome) hMSH2,hMLH1,hPMS2